Arrhythmogenic Right Ventricular Cardiomyopathy Puns

Hello meddit, I have to make a presentation about arrhythmogenic right ventricular cardiomyopathy and have some trouble finding reliable sources. Anyone any ideas? (I can use german, english and italian sources) Thank you in advance!

ECGs are here

I also posted this on r/medicine. Basically I admitted this pt for something completely unrelated. Saw that she has an ICD due to ARVD and was hoping to see some classic epsilon waves but came off a little disappointed. I know the diagnosis is challenging and based on multiple different criteria but I was wondering if any EP's here might clarify that a true epsilon wave has to be upright in the right precordial leads correct?

ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA Hugh Calkins, MD Current Problems in Cardiology Volume 38, Issue 3 , Pages 103-123, March 2013 http://www.cpcardiology.com/article/S0146-2806(12)00243-5/abstract

Hello,

I'm a 26 yo male ... followed up on my heart after my dad was diagnosed with amyloid cardiomyopathy, which turned out to be gene-negative (wild type TTR).

Incidentally, the attending cardiologists discovered that in a period of only 1 year, I lost 10% of my Ejection Fraction - from 60% to 50% - for an unknown reason.

I already had a diagnosis of extrasystole (premature ventricular, premature junctional) - could these frequent PVCs have caused the cardiomyopathy over time?

They suggested:
- viral infection

- adverse reaction to SARS-CoV-2 vaccination

- alcohol use (but I am not at all a heavy drinker)
- occupational exposure to a toxicant
- deconditioning, as the past year almost one year I've been sedentary due to inguinal hernia which is finally repaired and healed

- other, unknown reasons

I realize that 50% ejection fraction is very bad and some "progressive" cardiologists are calling it a symptom of early heart failure. Am I doomed?

https://www.ncbi.nlm.nih.gov/pubmed/32051229

Song JP1, Chen L2, Chen X2, Ren J2, Zhang NN2, Tirasawasdichai T3, Hu ZL2, Hua W2, Hu YR2, Tang HR4, Chen HV5, Hu SS1.

Abstract

Sudden death could be the first symptom of patients with arrhythmogenic cardiomyopathy (AC), a disease for which clinical indicators predicting adverse progression remain lacking. Recent findings suggest that metabolic dysregulation is present in AC. We performed this study to identify metabolic indicators that predicted major adverse cardiac events (MACEs) in patients with AC and their relatives. Comparing explanted hearts from patients with AC and healthy donors, we identified deregulated metabolic pathways using quantitative proteomics. Right ventricles (RVs) from patients with AC displayed elevated ketone metabolic enzymes, OXCT1 and HMGCS2, suggesting higher ketone metabolism in AC RVs. Analysis of matched coronary artery and sinus plasma suggested potential ketone body synthesis at early-stage AC, which was validated using patient-derived induced pluripotent stem cell-derived cardiomyocytes (iPSC-CMs) in vitro. Targeted metabolomics analysi

I was reading about some of my symptoms this morning and it matches almost exactly what it seems like is happening to me, so just wondering if anybody else has dealt with this same problem and if I stop drinking completely, does it ever get any better? Did I completely fuck up my heart beyond repair?

Source article

the former (HOCM) being a congenital condition in kids that causes syncope, early mortality, and hypertrophy of inter ventricular septum

the latter being concentric thickening of the ventricles to overcome increased preload.

also if anyone has a link, that would be great! thanks

It may seem a little dumb, but the doubt popped into my head. I'm not so sure, because there are still valves that are along the extension of the veins of the systemic circulation and maintain the flow, and maybe these impulses are the biggest force in this circulation, even because the LV systole has the help of gravity. I hope you guys help me with this!

In a UWorld question, this fact was mentioned:

Right ventricular hypertrophy (due to Eisenmenger syndrome) May lead to tricuspid regurgitation.

I thought AV valve regurgitations are due to ventricular DILATION, not concentric hypertrophy.

Any input is appreciated.

Hi, I have a question. I have my exam like in a few hours. Please help.

How is right ventricular pressure measured? There's a few options. The question goes like, "Right ventricular filling pressure is accurately measured by - a)PA catheter b)CV catheter c)femoral catheter d)None"

I hope it’s okay for me to post this here asking, but basically the title.

I’m a CVICU nurse primarily and I’ve always been curious why there was no way to calculate RVEF using an echo like we can for the left ventricle. I’ve asked the echo techs before but never really gotten an answer.

Bonus question: Do you think we will be able to in the future?

Edit: thank you for all the great responses!

During a lecture we have been shown a case of right ventricular hypertrophy as a consequence of COPD.

The problem is that I, a poor simple minded med student, had already ruled out a right ventricular hypertrophy after the ECG showed a cardiac axis of around 15 degrees. The enlargement was severe, so I can't even justify the lack of deviation as the hypertrophy not been significant enough.
I wonder if someone has an explanation; it's my first time facing cardiology so I must be missing something (though I wouldn't know where to look for an answer in this specific case)

My son is now 2 years old and this was the diagnosis during my congenital anomaly scan. At 3 months he had a Glenn Schunt, last year he got some coils, and in a few years is due for another surgery. Iirc his cardio told me he's only encountered this once before but unfortunately the baby didn't make it. But what about in other places? How often does this happen?

Edit: I'm not from the US, and am already aware of the statistics in my country, so our consulting cardiologist's experience has nothing to do with my question (cos some commented that we look for a more experienced doctor). Just want to know what it's like in other places.

I was in the ER for some vision loss and confusion the other day and they did and ECG and some blood draws. They said everything came back normal and so they weren’t sure what caused it.

However, flipping through my chart right now, it looks like they found a suggestion for a right ventricular conduction delay. I normally would shrug something the doctor cleared off, but my family has a history of hypertension and of heart disease.

I’m 23F, so I’m still young! But this is just a general question.

I was curious to see if any doctors could give me some insight to what is going on with my heart here. I am 22M and an elite level athlete. I had COVID back in December and after I recovered, my doc ordered an EKG and a Troponin blood test to see if COVID had affected my heart in any way. The EKG showed the Incomplete RBBB and borderline right ventricular hypotrophy. Troponin test did not raise any concerns whatsoever. I understand that these conditions are common in aerobic athletes.

The catch to all of this is that I have been experiencing chest pressure since mid December, shortly after I got the tests done. The first week after the tests the chest pressure felt like a burning sensation, particularly in the center of my chest. To describe it further, the burning is a fleeting sensation that lasts for a couple seconds and occurs multiple times a day. As of now, I do not feel the sensation as often but still occurs a couple times a week. I am getting an ECHO next week and my PCP thinks everything is alright but I am still concerned and would like some opinions on the matter.

Edit: I should also point out that when I lean back and stretch my arms up, my sternum feels like its ripping and that burning sensation is really prominent. I also have a dull pain in my left shoulder.

My son is now 2 years old and this was the diagnosis during the congenital anomaly scan. At 3 months he had a Glenn Schunt, last year he got some coils, and in a few years is due for another surgery. Iirc his cardio told me he's only encountered this once before but unfortunately the baby didn't make it. But what about in other places? How often does this happen?