Congenital hearing loss Puns

I've had congenital Sensorineural hearing loss since I was born (14 Now) and basically my dad says I can't do football or stuff where I get hit in the head because he says it makes my hearing worse. I've looked this up a bunch and haven't found anything saying that hearing loss gets worse from hits to the head. So is it true or not true?

Hi—

My kid was born with congenital CMV. She’s been diagnosed with “severe profound hearing loss” in one ear— and there’s a good chance she’ll lose hearing in the other ear over the next few years. She’s almost a month old.

I’m lost.

I’m looking for parents who have gone through similar circumstances. And/Or young adults who’ve experienced a life without sound.

Are there support groups for parents of kids with CMV? Broadly— or more specifically, any experience with antivirals?

We’re receiving a great deal of specialized medical care... and thankfully— she doesn’t show symptoms of some of the other more severe aspects of congenital CMV (microcephaly, liver disease, blindness, etc.).

—

As an aside, I’ve spent the last few days reading through this subreddit and r/deaf — I’ve learned a ton about this broader community in a short amount of time. That said— I hope this post is welcome here. It’s really a broad outreach, because I don’t know what I’m looking for.

Please no comments about bad breeding. That ship has sailed, we’re not returning her.

Our trainer noticed our puppy wasn’t reacting to the clicker, despite it being charged, or to a variety of other noises. She recommended getting her hearing checked which we did today.

There is nowhere in our state that does the BAER hearing test which is the gold standard and can actually quantify the amount of hearing loss. But our vet did basic hearing tests. Our puppy CAN hear, but not well and not certain noises. We know she can hear loud rumbly noises like cars and lawn mowers because they scare her (what we are working on with the trainer) and certain high pitched noises like certain squeakers and a sharp loud whistle, but us just talking to her? Nope. Softer noises like a clicker? Nope. Even clapping, she can’t really hear.

We’re not returning her to the breeder although our contract would allow us to. I’m mostly just wondering if anyone has experience raising a puppy with hearing loss. Any tips? Is she going to be able to do socialization activities like puppy playtime and group classes? Also can this impact socialization - she is pretty timid and I wonder if this is related at all. My research says deaf dogs can be more shy but she isn’t FULLY deaf.

We are at a loss. My wife is a SAHM and I work about an hour away from the house (small rural farming community where we live) and we found out that due to my income, we are not candidates for MedicAid (though it's only a small amount over my base pay). We know hearing aids are something you buy about every 5 years and that will add up. We HAVE to handle the hearing for our daughter (this will affect her learning and development drastically) and will do whatever we have to. We are looking for any other options that may be available for assistance in the expense.

Here's what we have come up with:

• Wife gets a job and we put the daughter into daycare where we can get her to pre-school, put the hearing aid on CC and pay off as we go (we have some room on CC's, but really been trying to NOT use them). Wife's income covers daycare and hearing.

• Asking my employer to DROP my wages to the mark. My Boss was baffled by this request, but if we can get EVERYTHING covered by dropping the ~3000 / year to get me to the cap, then it's more than a wash, right?

• Divorce - this blew me away to be a recommendation by my MOTHER of all people! Apparently divorcing will put the daughter into a completely different bracket and I suppose I pay child support? I freaked out a little when this was mentioned (by a wife sobbing uncontrollably) and told her - that is the dumbest idea I've ever heard.. Tonight my Mother will be getting a phone call.

We are still in "shell shock" right now finding out there's nothing to help with the cost of hearing aids, and I thought this would be a good place to help get grounded again..

Does anyone have any experience with this type of situation? Are there other options out there that we can peruse to help off-set the cost of these guys? We have been instructed it will be ~5k for the hearing aids.

UPDATE EDIT: We received word from our Audiologist that they reached out to a Hearing Aid manufacturer and they were able to procure her a free set of HA's! We were completely floored by their generosity!!

Thank you all for the advice! It's very much so appreciated!

Proof: http://imgur.com/qX6er

Those are hearing aids that I've had for a year- my second set. My backstory: I was born with what my audiologist calls "moderately severe" hearing loss. I can still hear some noise without hearing aids, but not very much. I taught myself to read lips at a young age since the only hearing aids I could receive were through my school to help make my learning process easier.

The reason I didn't receive hearing aids for so long? I had a single mother who was working her way through college so money was scarce and we couldn't find a audiologist in our area who would accept medicaid as a form of payment.

I'm also a huge gamer. I've played since I could hold a Nintendo controller in my hand.

Ask away!

This is an automatic summary, original reduced by 54%.

> There are more than 300 genetic defects that have been found to prevent the hair cells in the human inner ear, the sensory cells of the ear as it were, from working properly.

> Together with researchers at the Medical School in Harvard, Boston, Lukas Landegger of MedUni Vienna's Department of Ear, Nose and Throat Diseases has now succeeded, for the very first time, to repair this defect in an animal model - by using a modified, non-pathogenic adeno-associated virus, which is introduced into the ear by way of a "Trojan Horse" to deliver genes to restore the functionality of the damaged hair cells.

> "However, these electronic implants with their twelve electrodes cannot 100% replace the more than 3,000 hair cells in the inner ear, which give as much finer hearing," says Wolfgang Gstöttner, Head of the ENT Department at MedUni Vienna.

> Adeno-associated virus as a gene vector The commonest form of congenital deafness in children is due to the genetic mutation of GJB2 and GJB6. This mutation prevents the protein connexin 26, which is responsible for the cells in the cell complex of the inner ear, from working properly.

> This virus is infiltrated into the hair cells as a gene vector.

> What was surprising was that, in addition to the inner hair cells that are responsible for signal transduction, it was also possible to treat the 90% of outer hair cells, which perform an important amplification function in the inner ear and have hitherto been virtually inaccessible for gene therapy.

Summary Source | FAQ | Theory | Feedback | Top five keywords: cell^#1 hair^#2 ear^#3 hearing^#4 virus^#5

Post found in [/r/science](ht

Wife has bad hearing loss and I keep telling her to go to an audiologist. The problem is that she won't hear anything about it!

I found out in my personal experience that even though an ENT center or Audiologist tested me in their office and said I had perfect hearing (actually bragged that I had great hearing) and no indication of hearing loss that it wasn’t an accurate assessment. I say this because I have an extensive background in audio. One of my jobs or tools of my trade is to run frequency sweeps from low to high that go below and above what humans typically hear. Prior to my high frequency tinnitus I could hear up to about 13,500khz. My wife and younger people can typically hear even higher frequencies. My wife can hear up to about 16,000khz. The high end of our hearing does deteriorate with age and is common. However, as soon as my high pitched tinnitus started I was already familiar with frequency range my high pitched tinnitus was in.

I used my tone generator to test this theory and I could sweep up to the frequency I could hear my ringing at and it was 10,800khz. Also, coincidentally that’s where my hearing now appeared to stop. So I can no longer hear up to 13,500khz. So what does this mean? Well, in my day to day and for everyone else absolutely nothing because it doesn’t fall down into the frequency range that would cause any issues for anyone. Frequencies or pitches that high are not common things we notice in our day to day and human speech is well below that. So while a trip to your ENT specialist / Audiologist could show no signs of hearing loss there can still be hearing loss that occurred that they’re not aware of. After my testing session at the clinic near me I realized that their tests aren’t even designed to test for that.

This whole experience has shown me just how ill equipped ENT / Audiologist can be when it comes to tinnitus and how lacking tinnitus research actually is. The tough part is, if you haven’t tested your hearing as far as the frequency spectrum pre any high frequency hearing loss then how would you know if you ever lost any part of your upper frequency to begin with, especially if it’s so high that it’s something you wouldn’t notice in your day to day?

I would have never noticed that I lost that range had it not been for the type of work I do. With everything I’ve read on tinnitus (since mine started in July 2021) it appears that there are probably multiple causes and that not all tinnitus is the same. This also has me wondering how research is being done because if they are lumping all tinnitus in the same category an

Hi, I am new here. I am in the process of freezing my eggs, so I hope this post is ok because I am technically not doing IVF.

Since my egg retrieval in November, my mild but constant hair loss (head hair) because of NCAH has considerably increased. [I wasn't in treatment before egg freezing because the diagnosis was only discovered during the blood work for my initial consult]

1. Is this temporary? Will my hair grow back/become thicker again?
2. Is there anything I can do to prevent hair loss during my next stimulation and egg retrieval? Like go on a certain medication or something?

I know these come up now and then, but seriously, please protect your ears when practicing or going to shows or doing anything that's moderately loud or more. Get some good ear protection and be blown away by how things actually sound BETTER, not worse. They stop you from overdriving your hearing so much, so everything is clearer and amazing. A trillion times over, it is worth it to buy some professional ear plugs and wear them any time stuff is gonna be loud. I spent so many years blasting my ears with headphones, at shows, in cars, and standing next to drummers and it definitely comes back to bite you in ways you wouldn't expect.

Probably the most profound way is that I just really can't stand trying to hold a conversation with someone. Hearing loss can make it so that you have a really really hard time distinguishing between similar consonants, so your brain just hears gibberish because it doesn't make any sense until you take a second and use context to put everything together...which can be super dodgy and lead to embarrassing misunderstandings because you've just been standing there smiling and trying to figure out what this person has been telling you and you end up just laughing while you figure it out...then figure out someone just died or something.

Aside from awkward conversations, some people just can NOT fathom that they need to speak more loudly and clearly because there's background noise so it becomes a continuing game of "I'm sorry, what?", "What was that?", "One more time?", "Come again?". At some point, the person either gets somehow offended or just frustrated that you keep on telling them over and over that you can't hear them, and says it doesn't matter and drops it (which you'll never know wtf "it" was because you can't hear shit!). I grow weed for a living, so we have like 20 fans, 4 huge A/C units, 2 industrial dehumidifiers, and usually a speaker blasting some music running at all times in a room and keeping it around 70-72 decibels. People love getting high and chatting; hell, I love getting high and chatting....but hearing loss makes it so that I have approximately zero chance of understanding what someone is saying with that kind of background noise so you just have to avoid conversation.

From there, forget about trying to have group conversations, especially if there's music in the background. Once you get lost, all you can do is watch other people's reactions and hope you can figure out the direction of conversation and

I have had mild-moderate hearing loss since I was 3 months old. I have difficulty understanding people if they are far away from me but can understand 3-4 people close up if there is no cross talk / mumbling. But it can still be a struggle to understand what people are saying especially if they use big words, even words that I understand.

Now I have always been a smart, creative person in spite of my hearing loss. I could read really well at a young age, and do math and I get frequently told that I'm really insightful. However, the same people who tell me these things also have a tendency to treat me like I'm dumb, even when they know I have hearing difficulties.

I can kind of understand why they would think this- because most people think that hearing loss is measured by how many words you are able to understand. So according to their idea of what hearing loss is like, it's like you misunderstand 15% of words if mild. Therefore the other 85% of words are heard perfectly with no problems.

As we all know, this ignores the fact that ALL sound is distorted when you have hearing loss, and HOH have to put in effort to understand people regardless of what's being said. But some words are easier to figure out through context. So if someone is talking to you but they are using more familiar, easy-to-understand words, it is easier to piece together what they saying than if they use big words.

From the perspective of a hearing person who thinks hearing loss is "certain words are muffled, others are fine", it leads them to hold the impression that the person who doesn't understand them - doesn't understand uncommon words. If they are talking to someone and they understand a long sentence "Can you get this box for me right now?" really fast, but not a sentence like "Help me assemble this shelf", it may lead them to think: oh they don't know about shelves or the process of building, but they do know how to retrieve things.

Which brings me to my next point: In my teenage years I realized that if I acted like I was dumb / mentally challenged, people would be less likely to treat me like I was dumb, rather socially awkward because their expectations would be lowered. And then I'd reveal offhand all the things I did know, and I'd play it off like, "Wow, I'm smart, really? I didn't know!" So if someone talked to me I'd respond back "Pree-tty good how about you?" but then in class they would see that I was good at math /reading, and then they would realize that I wasn'

I (37F) just had my 2 year hearing test since getting hearing aids in 2020, luckily just before masks became a thing. My audiologist told me that in his experience, a hereditary hearing loss continues to decline; he’s only seen 1-2 people who’s loss stopped. So now I’m completely freaked out that I won’t be able to hear people speak eventually.

I’m sure my story is similar to many, unknowingly struggled with hearing loss all my life and have had tinnitus as long as I can remember.

Hello all,

I contracted COVID at the beginning of the month and immediately lost hearing in my right ear. I was sure it was congestion so I wasn’t worried about it, but now that my symptoms are like 95% gone, the hearing hasn’t improved.

This is causing a problem in university. Before I had some trouble with “mumbling” (even with masks) but I was usually able to understand most things. Now I can’t understand any teachers with accents most of the time (wasn’t a real issue before, or I could catch the gist of what they were saying) or I can barely hear them. I’ve moved to the front row in all my classes.

Anyway, I was wondering if it would be best to go to an ENT doctor first or an audiologist? I’m not sure if I can get any accommodations because I don’t have a record for anything, but does anyone have any advice? I’m really worried about this affecting both my school work and job (I’m a waitress and am having a hard time hearing my name called to food run and talking to tables).

Any advice is greatly appreciated.